Description of target: This gene encodes a lysosomal serine protease that cleaves n-terminal tripeptides from protein substrates. the encoded preproprotein undergoes autocatalytic processing to generate a mature enzyme. mice lacking the encoded protein exhibit a progressive neurodegeneration and a greatly shortened lifespan. at the cellular level, mice lacking the encoded protein exhibit accumulation of autofluorescent lipopigments. mutations in the human ortholog of this gene cause classical late-infantile neuronal ceroid lipofuscinosis.;Species reactivity: Mouse;Application: ;Assay info: Quantitative Sandwich ELISA;Sensitivity: <0.055ng/mL
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Număr Catalog 247-OKDD00789CategorieAfaceri și industrie > Știință și laboratorFurnizorAviva Systems BiologyGentaurDimensiune96 WellsTipsingle
